Amelogenesis Imperfecta: No Enamel on Teeth

Healthy enamel acts as a protective buffer against tooth decay. This hard exterior shields the inner layers of the teeth from the effects of acids and plaque. It also prevents tooth sensitivity that can be caused by extremely hot or cold foods and beverages.

This condition can affect baby teeth and adult (permanent) teeth. Amelogenesis Imperfecta (AI) is caused by mutations in genes that can be passed down in families, but new gene alterations can occur even without a family history of the condition.

Amelogenesis imperfecta affects the appearance and strength of teeth. Teeth appear small, discolored, pitted, and prone to breaking. There are four classifications of amelogenesis imperfecta, with each presenting various symptoms:

• Hypoplastic: This type of AI is characterized by small or normal dental crowns (the top of the teeth), misalignment in the upper and lower teeth, and tooth discoloration. The enamel can be thin, smooth, or normal, with grooves, lines, and/or pits.
• Hypomaturation: Type II AI also affects teeth alignment. People with this type of amelogenesis imperfecta often have an open bite where the upper front teeth and lower teeth don't touch when the mouth is closed. The tooth's surface may have a creamy white or yellow-brown, rough texture that may be tender or sore. Generally, the enamel will be normal in thickness but may look chipped or scraped.
• Hypocalcified: Type III is also associated with an open bite and creamy white to yellow-brown tooth surface that may be tender and sore. Like type II AI, people with type III tend to have chipped tooth enamel.
• Hypomaturation/Hypoplasia/Taurodontism: Type IV, also known as enamel hypomaturation or taurodontism, occurs when teeth have a white to yellow-brown look, with spots. The enamel is thinner and softer than normal.

Teeth with thin, soft, or no enamel are at risk of early tooth decay, gum disease, and tooth sensitivity. Healthy enamel protects your teeth against these dental issues. Without this buffer, the sensitive parts of teeth are left exposed. Dentin is the second layer of the tooth, which contains thousands of microscopic tubules that lead to the tooth's pulp (which consists of nerve endings and blood vessels). When these parts of the tooth are exposed to hot or cold foods and beverages, it results in uncomfortable pain.

Treatment will depend on the type of amelogenesis imperfecta you are diagnosed with. Your dental professional may recommend restorative treatments like sealants, crowns, implants, and bonding. These will restore the size, shape, strength, and appearance of the affected teeth. Malocclusion (an abnormal alignment of the upper and lower teeth when the jaws are closed) is a common characteristic of AI. People with AI should see an orthodontist who can advise about treatment that can correct a misaligned bite.

Teeth with no enamel is a condition that can affect you or your child's self-confidence, as it impacts the appearance and functionality of the teeth. If you or your child experience a rough tooth surface, discoloration, and sensitivity, you shouldn't hesitate to speak to your dental professional. They can find the best treatment options to improve your oral health and give you confidence in your smile!

Oral Care Center articles are reviewed by an oral health medical professional. This information is for educational purposes only. This content is not intended to be a substitute for professional medical advice, diagnosis or treatment. Always seek the advice of your dentist, physician or other qualified healthcare provider.