Dentin dysplasia (DD) is a rare, inherited condition. It affects the formation of the dentin, which is the mineralized portion of the tooth underneath the enamel and cementum. The condition is characterized by abnormal dentin and root development, resulting in atypical tooth formation.
This condition is extremely rare, affecting 1 person in every 100,000, according to the Journal of Oral and Maxillofacial Radiology. Considered an autosomal dominant trait, it can occur in baby or permanent teeth as either type I or II. Type I, known as radicular dysplasia, refers to the roots of teeth. Type II, known as coronal dysplasia, refers to the crown of the teeth, which is the part visible above the gumline.